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KMID : 0387820060130020238
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Clinical Pediatric Hematology-Oncology
2006 Volume.13 No. 2 p.238 ~ p.242
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A Case of Pulmonary Blastoma with Rhabdomyoblastic Differentiation
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Ryu Eo-Young
Jang Sun-Hwa
Yeom Jung-Sook
Park Eun-Sil
Seo Ji-Hyun
Lim Jae-Young
Park Chan-Hoo
Woo Hyang-Ok
Youn Hee-Sang
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Abstract
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ulmonary blastoma is a rare primary malignant neoplasm of lung with poor prognosis in children. Histologically, it is composed of epithelial and mesenchymal element: the latter may show various pattern of differentiation toward mature tissue, such as cartilage, smooth muscle, and bone. Rhabdomyoblastic differentiation in pulmonary blastoma is quite rare. In the literature, only eight cases have been reported including a Korean patient. Complete surgical removal is always required for the treatment and chemotherapy and radiotherapy are needed as adjuvant therapy. We report a case of pulmonary blastoma with rhabdomyoblastic differentiation treated with surgical removal, chemotherapy (vincristine, actinomycin D, cyclophosphamide, adriamycin) and radiotherapy.
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KEYWORD
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Pulmonary blastoma, Rhabdomyoblastic differentiation
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